五、治疗

五、治疗

颈部以下的轻度融合可以进行非手术的治疗方案,定期检查减少剧烈的接触性的运动。对于有持续性神经疼痛,脊髓病变,肌无力和脊柱不稳定的患者可以考虑手术治疗。

参考文献

[1]图示ota S,Zagar I,Delimar V,et al.Klippel-Feil syndrome misdiagnosed as spondyloarthropathy:Casebased review[J].Rheumatology International,2019,39(9):1655-1660.

[2]Pirino A,Sotgiu M A,Cosmi E,et al.Association of Klippel-Feil syndrome,Dandy-Walker malformation,spina bifida:A case report[J].Radiology Case Reports,2019,14(3):415-418.(https://www.daowen.com)

[3]Guo X Y,Zhu N,Hao D J.Rare hereditary klippel-feil syndrome and Arnold-chiarimalformation caused by cervical spondylotic myelopathy[J].World Neurosurgery,2019,125:126-128.

[4]Dauer M V P,Currie P D,Berger J.Skeletal malformations of Meox1-deficient zebrafish resemble human Klippel-Feil syndrome[J].Journal of Anatomy,2018,233(6):687-695.

[5]曾实,许民辉,徐伦山,等.Klippel-Feil综合征伴颅颈交界区畸胎瘤1例报道并文献复习[J].重庆医学,2018,47(13):1838-1840.

(邢向辉 臧睿觉)