五、治疗
(一)一般治疗
本病尚无特殊治疗,一般对症处理。
抑制内分泌腺体功能亢进,纠正内分泌异常。骨病可采用刮除术、处理骨折、预防畸形。骨病引起的特殊并发症如颅底或眼眶骨纤维化引起视神经孔狭窄导致视力障碍、甚至失明,可以试用手术矫治。同时应当加强护理,避免外伤发生骨折,色素斑一般不需要处理。
(二)口腔颌面部异常相关的治疗建议
口腔颌面的治疗主要针对伴有颌骨变形,牙移位及错
畸形的患者,可以通过口腔颌面外科、口腔正畸科等多学科协作改善患者错
畸形以及面型。
参考文献
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(贺智凤 韩生伟 王志勇)