三、发明内容

三、发明内容

针对上述现有技术存在的缺陷或不足,本发明的目的在于,提供一组用于检测血友病患者的FⅧ/FⅨ基因突变的引物,并利用引物进行血友病病因学分类。

为了实现上述任务,本发明采取如下的技术解决方案:

一组FⅧ/FⅨ基因突变引物在制备血友病病因学分类试剂中的用途,其特征在于,所述的引物为8对F9引物,39对、22倒位3条、1倒位4条F8引物,其中:

1.8对F9引物的序列如下:

HB-1F:CCCATTCTCTTCACTTGTCC;

HB-1R:CCTAGCTAACAAAGAACAGT;

HB-2+3F:AGAGATGTAAAATTTTCATGATGTT;

HB-2+3R:GCAGAAAAAACCCACATAAT;

HB-4F:CTACAGGGGAGGACCGGGCATTCTA;

HB-4R:AGTTTCAACTTGTTTCAGAGGGAA;

HB-5F:CATGAGTCAGTAGTTCCATGTACTTT;

HB-5R:TGTAGGTTTGTTAAAATGCTGAAGTT;

HB-6F:TTTAAATACTGATGGGCCTG;

HB-6R:GTTAGTGCTGAAACTTGCCT;

HB-7F:TAGGTCAGTGGTCCCAAGTAGTC;

HB-7R:GTCCCCCACTATCTCCTTGA;

HB-8-1F:TAAGAATGAGATCTTTAACA;

HB-8-1R:CTAAGGTAGTGAAGAACTAA;

HB-8-2F:GAAGAGTCTTCCACAAAGGG;

HB-8-2R:AAGATGGGAAAGTGATTAGTTA;

2.39对F8引物的序列如下:

HA-1F:gtagcgcgacggccagtAGCATCACAACCATCCTAAC;

HA-1R:cagggcgcagcgatgacGCACATCCAGTGGGTAAAGT;

HA-2F:TGGAAGCATTACTTCCAGCT;

HA-2R:AACTGAAACCTCAAGATTGG;

HA-3F:TGCTTCTCCACTGTGACCT;

HA-3R:ATCTAGTAAATGTAAGAAATACA;

HA-4F:AGCCCACAGATTTGAAGAGG;

HA-4R:ACGTTGCTGTGAGCCGAGAT;

HA-5F:CTTACTGTCAAGTAACTGATG;

HA-5R:CTTCATTCCTGAACAGTAATG;

HA-6F:TCCCACTTATTGTCATGGAC;

HA-6R:TACAGAACTGGTGCTGAA;

HA-7F:gtagcgcgacggccagtATAATGTCCCCTTCAGCAAC;

HA-7R:cagggcgcagcgatgacAGCCCAATGTTCTTGATAAA;

HA-8F:CCATATAGCCTGCAGAACAT;

HA-8R:CTGATGCTCAGCTATGTTAG;

HA-9F:gtagcgcgacggccagtCGAGTTTAGTGGGTGACATT;

HA-9R:cagggcgcagcgatgacTTTAGAGTTGGATTTGAGCC;

HA-10F:CTAGCCTCAAATTACTATAATG;

HA-10R:ACTTTAGACTGGAGCTTGAG;

HA-11F:gtagcgcgacggccagtAAGGGGACATACACTGAGAA;

HA-11R:cagggcgcagcgatgacGACACTTTCACAGTCAACCG;

HA-12F:TGCCATCGCTTTCATCATAG;

HA-12R:CATTCATTATTATCTGGACATCAC;

HA-13F:TTCCTGGGAATAAGATAATGG;

HA-13R:AGCATACGAATGGCTAGTGA;

HA-14aF:ACAGGCATAGTACAACAGCA;

HA-14aR:CTTGGCTATTCATTAAACCTG;

HA-14bF:TCCATCAGACAATTTGGCAG;

HA-14bR:CTACATTTTGCCTAGTGCTC;

HA-14CF:gtagcgcgacggccagtCACTGTATGTATCTGAGGCA;

HA-14CR:cagggcgcagcgatgacAGACAAACAAAACTTCCAAT;

HA-14dF:ATCTTCCAGCAGCATCTTAT;

HA-14dR:CCTCTACCCTCTTGTAAACC;

HA-14eF:gtagcgcgacggccagtGGATGACACCTCAACCCAGT;

HA-14eR:cagggcgcagcgatgacCCTTCCACGAGATCCAGATG;(https://www.daowen.com)

HA-14fF:gtagcgcgacggccagtTOCCTAOGGAAACTAGCAATG;

HA-14fR:cagggcgcagcgatgacTCACAAGAGCAGAGCAAAGG;

HA-15F:gtagcgcgacggccagtATTCCACTGTCCTTAACTCACCA;

HA-15R:cagggcgcagcgatgacACAAAACCCCAGCTTTCATG;

Ha-15F:gtagcgcgacggccagtAAAAATTTCCAAAAGTGGGA;

Ha-15R:cagggcgcagcgatgacTGGCAAGAGTATTTCAAGGA;

HA-16F:gtagcgcgacggccagtGAACCAGAGTGGATTTCTCA;

HA-16R:cagggcgcagcgatgacGAACCAGAGTGGATTTCTCA;

HA-17F:TGTCATTACTGACTGGAATCT;

HA-17R:CACTCCCACAGATATACTCT;

HA-18F:gtagcgcgacggccagtCCCAGTGCCTAGACCATTTAA;

HA-18R:cagggcgcagcgatgacTTGATCCAGGGACTTGAACAT;

HA-19F:CGCATAAACCAATGTATCTCATGCTC;

HA-19R:TCCTGACACAAGCAACCATTCC;

HA-20F:GACGTTCTCCCATTTTCATTG;

HA-20R:GGATTCATTATCTGAGATTCTCCACCAG;

HA-21F:CAGCTTAGATTAACCTTTCTC;

HA-21R:GAGTGAATGTGATACATTTCC;

HA-22F:TCAGGAGGTAGCACATACAT;

HA-22R:GTCCAATATCTGAAATCTGC;

HA-23F:GTCTTATGTAGATGTTGGATG;

HA-23R:AGTCTCAGGATAACTAGAACA;

HA-24F:GCTCAGTATAACTGAGGCTG;

HA-24R:CCCATAACCAAACTTCCTTGACAC;

HA-25F:AGTGCTGTGGTATGGTTAAG;

HA-25R:TTGCTCTGAAAATTTGGTCATA;

HA-26AF:gtagcgcgacggccagtCTCTGAGAGGCCTAACTTTT;

HA-26AR:cagggcgcagcgatgacATCCTGGACTACTGGAAACA;

HA-26bF:gtagcgcgacggccagtGGAGAAACCTGCATGAAAGC;

HA-26bR:cagggcgcagcgatgacTTGGCCATCACAAATTTCAA;

HA-26cF:gtagcgcgacggccagtTGCAAATGTGCATTTTTCTGA;

HA-26cR:cagggcgcagcgatgacCCTCCAGCCCCCTTTACTAT;

HA-26dF:gtagcgcgacggccagtCCACCCCCATAAGATTGTGA;

HA-26dR:cagggcgcagcgatgacCTGAAGAAACCAGCAGGAAAA;

HA-26EF:gtagcgcgacggccagtTCTTGCTATTCAGTGCCCCTA;

HA-26ER:cagggcgcagcgatgacGCTTGACCCTTATCTGACCTCTT;

HA-P1F:gtagcgcgacggccagtACAGAAAGAAGCAGGTGGAG;

HA-P1R:cagggcgcagcgatgacGAAGAGGGTTGGAGTAGGC;

HA-P2F:gtagcgcgacggccagtGAGGGATGGAGAAGTCAAAGTG;

HA-P2R:cagggcgcagcgatgacGAAATCTGGGGGAAAGGTGT;

HA-P3F:gtagcgcgacggccagtACCTCAACACTTGCTATTTC;

HA-P3R:cagggcgcagcgatgacAGTGTTTATCAAAGGGGCT;

3.22倒位3条F8引物的序列如下:

HA-P:TGCCTGTCCATTACACTGATGACATTATGCTGA;

HA-Q:TACAACCATTCTGCCTTTCACTTTCAGTGCAATA;

HA-B:CCAAACTATAACCAGCACCTTGAACTTCCCCTCTCA;

4.1倒位4条F8引物的序列如下:

HA-9F:GTTGTTGGGAATGGTTACGG;

HA-9cR:CTAGCTTGAGCTCCCTGTGG;

HA-intlh-2F:GGCAGGGATCTTGTTGGTAAA;

HA-intlh-2R:TGGGTGATATAAGCTGCTGAGCTA。

经申请人的试验证明,上述用于检测血友病患者的FⅧ/FⅨ基因突变的引物可以用于血友病病因学分类的应用。

所述血友病病因学分类的步骤如下:

(1)用MC-1000血凝仪检测患者的FⅧ/FⅨ:C,确定是否为FⅧ/FⅨ缺乏。

(2)8对F9引物,以及39对、22倒位3条、1倒位4条F8引物,用ABI 3100基因分析仪测序技术及优选多重与倒转环化PCR扩增技术检测患者的FⅧ/FⅨ基因突变;继用改良Nijmegen法检测患者的FⅧ/FⅨ:Ab。

(3)将检测结果分类为:血友病患者与其母亲的FⅧ/FⅨ基因均发生突变,而且突变的位点及类型完全相同,则为先天遗传性;血友病患者的FⅧ/FⅨ基因突变,而其母亲的FⅧ/FⅨ基因正常,且无家族遗传史,则为先天非遗传性;血友病患者及其母亲的FⅧ/FⅨ基因均正常,且无家族遗传史,血友病患者无既往异常出血史,但FⅧ/FⅨ:Ab检测常为阳性,则为后天获得性。

根据血友病病因学分类,可以应用非因子药物对血友病进行治疗,可使血友病患者由重型转变为中型,轻型,后天获得者FⅧ/FⅨ:C可恢复正常,进一步验证本发明的血友病病因学分类方法确切、可靠,为预防血友病出血和避免残疾,开辟了一条新思路、新途径。